Sjögren sendromu (sicca sendromu), bir otoimmun hastalıktır (kronik otoimmun sialadenit). SLE’den sonra en sık görülen bir otoimmun hastalıktır. 30 yaş üzeri kadın hastalar görece daha fazladır; ailesel yatkınlık gösteren olgular vardır. Hastaların tükürüklerinde duktus epitel hücrelerine karşı oluşmuş otoantikorlar (anti-Ro/SSA ve anti-La/SSB) bulunur.[1][2][3][4][5][6]
Aoun G, Nasseh I, Berberi A. Evaluation of the oral component of Sjögren's syndrome: An overview. Journal of International Society of Preventive & Community Dentistry, 6(4):278-284, 2016
Manzo C, Kechida M. Is primary Sjögren's syndrome a risk factor for malignancies different from lymphomas? What does the literature highlight about it? Reumatologia, 55(3):136-139, 2017
Both T, Dalm VA, van Hagen PM, van Daele PL. Reviewing primary Sjögren's syndrome: beyond the dryness - From pathophysiology to diagnosis and treatment. International Journal of Medical Sciences, 14(3):191-200, 2017
Ferro F, Marcucci E, Orlandi M, Baldini C, Bartoloni-Bocci E. One year in review 2017: primary Sjögren's syndrome. Clinical and Experimental Rheumatology, 35(2):179-191, 2017