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特发性间质肺炎(Idiopathic interstitial pneumonia,简称IIP),又称非感染性肺炎(noninfectious pneumonia)[1],属于一种间质性肺病。该疾病通常侵袭肺间质,有些也会侵袭气道(例如Cryptogenic organizing pneumonitis),IIP可分为七个亚型。
IIP的分类相当复杂[2],须结合临床观察、影像学,以及病理学[3][4]才能确诊。
其中寻常性间质性肺炎为最常见的一种亚型[7]。
Table 1: Development of the (histologic) idiopathic interstitial pneumonia classification
Leibow et al. (1969) | Katzenstein (1998)[8] | ATS/ERS (2002)[6] | |||||||||||||||||||||||||||
UIP | UIP | ||||||||||||||||||||||||||||
UIP | DAD | DAD | |||||||||||||||||||||||||||
NSIP | NSIP | ||||||||||||||||||||||||||||
DIP | DIP/RB | DIP | |||||||||||||||||||||||||||
RB | |||||||||||||||||||||||||||||
BIP | OP | OP | |||||||||||||||||||||||||||
LIP | (LPD) | LIP | |||||||||||||||||||||||||||
GIP | (HMF) | (HMF) | |||||||||||||||||||||||||||
UIP=usual interstitial pneumonia; DAD=diffuse alveolar damage; NSIP=non-specific interstitial pneumonia; DIP=desquamative interstitial pneumonia; RB=respiratory bronchiolitis; BIP=bronchiolitis obliterans interstitial pneumonia; OP=organizing pneumonia; LIP=lymphoid interstitial pneumonia; LPD=lymphoproliferative disease (not considered a diffuse lung disease); GIP=giant cell interstitial pneumonia; HMF=heavy metal fibrosis, no longer grouped with diffuse lung disease
Lymphoid interstitial pneumonia was originally included in this category, then excluded, then included again.[9]
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