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Riocht nuair nach féidir le colainn duine crapadh na matán deonach (sómatach) a choinneáil go leanúnach. Tarlaíonn sí de bharr uathantashubstaint ar leith a chuireann bac ar ghníomhú na néar-ríog luadrach a chuireann tús le crapadh na matán. Tagann tuirse go tapa ar na matáin, ach tagann siad chucu féin tar éis tréimhse suaimhnis.[1]
Cineál | neuromuscular junction disease (en) , autoimmune disease of musculoskeletal system (en) , immune-mediated acquired neuromuscular junction disease (en) , neamhord imdhíonachta, autoimmune disease of peripheral nervous system (en) agus galar |
---|---|
Speisialtacht leighis | néareolaíocht |
Cóireáil chliniciúil | |
Cógais pyridostigmine (en) , neostigmine (en) , cyclosporine (en) , (RS)-cioglafosfaimíd, prednisone (en) , azathioprine (en) , rituximab (en) , eculizumab (en) , mycophenolate mofetil (en) , prednisolone (en) , tacrolimus (en) , distigmine (en) agus pyridostigmine (en) | |
Pataigineas | |
Cúis ghéiniteach | TNIP1 agus CTLA4 |
Aicmiú | |
ICD-10 | G70.0 agus G70.00 |
ICD-9 | 358.00 agus 358.0 |
Acmhainní seachtracha | |
OMIM | 254200 |
DiseasesDB | 8460588 |
MedlinePlus | 000712 |
eMedicine | 1171206, 793136, 261815 agus 1216417 |
Patient UK | myasthenia-gravis-pro |
MeSH | D009157 |
Orphanet | 589 |
UMLS CUI | C1260409, C0751340, C0751339 agus C0026896 |
DOID | DOID:437 |
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